noncompact myocardium of the left ventricle

The article presents the clinical case of a 28-year-old female patient who was diagnosed with a noncompact myocardium of the left ventricle. The disease debuted with clinical signs of cardiac rhythm disturbance, according to long-term monitoring of electrocardiogram results a ventricular extrasystole equivalent to Lown 4b was detected. On echocardiography, a sharp decrease in the ejection fraction of the left ventricle was of particular significance .A diagnosis was made after magnetic resonance imaging of the heart, the presence of two layers of myocardium was detected: compact and noncompact layer, the latter exceeding the former in thickness greater than two times. The patient was recommended slow titration of  a dose of angiotensin-converting enzyme inhibitors up to the maximum tolerable dose under the control of blood pressure; addition  of anticoagulants on the basis of primary prevention of thromboembolic complications; elective implantation of a bi-chamber artificial cardioverter-defibrillator for the primary prevention of sudden cardiac death.